Pemphigus erythematosus associated with anti-DNA antibodies and multiple anti-ENA antibodies: a case report.
نویسندگان
چکیده
Pemphigus erythematosus (PE) is an autoimmune blistering disease combining features of pemphigus foliaceus (PF) and systemic lupus erythematosus (SLE). We report a case of PE associated with anti-double-stranded DNA (anti-dsDNA), anti-Smith (anti-Sm), anti-Ro (anti-SSA), and antiribonucleoprotein (anti-RNP) antibodies. This case required extensive immunosuppressive therapy. We treated our patient with a combination of systemic steroids, intramuscular gold injections, azathioprine, and hydroxychloroquine. The patient's response was complete remission--evaluated clinically, serologically, and immunohistochemically.
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ورودعنوان ژورنال:
- Cutis
دوره 71 4 شماره
صفحات -
تاریخ انتشار 2003